Iberoamerican Journal of Medicine
Iberoamerican Journal of Medicine
Case Report

A rare case of persistent urogenital sinus in an adult woman associated with unilateral rudimentary horn with ipsilateral renal agenesis and contralateral dermoid cyst

Un caso raro de seno urogenital persistente en una mujer adulta asociado a cuerno rudimentario unilateral con agenesia renal ipsilateral y quiste dermoide contralateral

Mohamed Ibrahim Amer

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Persistent urogenital sinus (PUGS) is an uncommon developmental cloacal anomaly, with Incidence of 0.6 in 10000 female births. Herein we depict the case of a 22-year of age lady who presented with Infertility for 16 months with dyspareunia and was found to have Persistent urogenital sinus associated with other urogenital anomalies as unilateral rudimentary horn with ipsilateral renal agenesis and contralateral dermoid cyst. The patient was successfully treated with the excision of the sinus, the rudimentary horn and the dermoid cyst.


Urogenital sinus; Renal agenesis; Rudimentary horn


El seno urogenital persistente (PUGS) es una anomalía cloacal del desarrollo poco común, con una incidencia de 0,6 en 10000 nacimientos de mujeres. Aquí representamos el caso de una señora de 22 años que presentó Infertilidad durante 16 meses con dispareunia y se encontró que tenía seno urogenital persistente asociado con otras anomalías urogenitales como cuerno rudimentario unilateral con agenesia renal ipsilateral y quiste dermoide contralateral. El paciente fue tratado con éxito con la escisión del seno, el cuerno rudimentario y el quiste dermoide.

Palabras clave

Seno urogenital; Agenesia renal; Cuerno rudimentario


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