Iberoamerican Journal of Medicine
https://iberoamjmed.com/article/doi/10.5281/zenodo.4011601
Iberoamerican Journal of Medicine
Case Report

Cutis Verticis Gyrata Secondary to Cerebriform Intradermal Naevus: A rare entity and its Management

Jia Yuan Lee, Shawatul Akhma Harun Nor Rashid, Wan Azman Wan Sulaiman, Nor Hayati Yunus, Ikmal Hisyam Bakrin

Downloads: 2
Views: 402

Abstract

Cutis verticis gyrata (CVG) is a rare skin disorder characterised by thick skin folds and grooves, resembling the gyri and sulci of the cerebral cortex. It can be classified as primary essential, primary non-essential and secondary CVG. The rarity of the condition poses a challenge in the diagnosis and ultimately requires good communication between the clinician and the dermatopathologist for diagnosis. Many names have been given to the condition, including Robert-Unna syndrome, cutis verticis plicata, paquidemia verticis gyrata, cutis sulcata, cutis striata or “bulldog” scalp syndrome. To date, the treatment is still limited to plastic surgeons with excision of the folds, scalp reduction and reconstruction.
In this article, we are sharing a rare case and the surgical management of a middle age gentleman with cutis verticis gyrata secondary to cerebral intradermal nevus (CIN) over his occipital scalp.

Keywords

Cutis verticis gyrata; Cerebriform intradermal nevus; Bulldog scalp syndrome

References

1. Larsen F, Birchall N. Cutis verticis gyrata: three cases with different aetiologies that demonstrate the classification system. Australas J Dermatol. 2007;48(2):91-4. doi: 10.1111/j.1440-0960.2007.00343.x.
2. Tucci A, Pezzani L, Scuvera G, Ronzoni L, Scola E, Esposito S, et al. Is cutis verticis Gyrata-Intellectual Disability syndrome an underdiagnosed condition? A case report and review of 62 cases. Am J Med Genet A. 2017;173(3):638-46. doi: 10.1002/ajmg.a.38054.
3. El-Husseiny M, Yarrow J, Moiemen N. Primary cutis gyrata: Review of literature and a successful new surgical approach. Eur J Plast Surg. 2010;33(3):153-7. doi: 10.1007/s00238-009-0383-y.
4. Beier JP, Kneser U, Horch RE. Surgical treatment of facial cutis verticis gyrata with direct excision. J Cutan Med Surg. 2007;11(1):4-8. doi: 10.2310/7750.2007.00003.
5. Taha HM, Orlando A. Butterfly-shape scalp excision: a single stage surgical technique for cutis verticis gyrata. J Plast Reconstr Aesthet Surg. 2014;67(12):1747-9. doi: 10.1016/j.bjps.2014.07.039.
6. Zhang MJ, Sun ZY, Liu Y, Wu SM, Lu KH. Rare giant secondary cutis verticis gyrata. J Plast Surg Hand Surg. 2011;45(4-5):212-4. doi: 10.3109/02844311.2010.488883.
7. Mutlu OO, Colak O, Canli M, Akcay A. Scalp Reconstruction With Free Latissimus Dorsi Flap in a Patient With Giant Cutis Verticis Gyrata. J Craniofac Surg. 2016;27(6):e553-e554. doi: 10.1097/SCS.0000000000002862.
8. Orkin M, Frichot BC 3rd, Zelickson AS. Cerebriform intradermal nevus. A cause of cutis verticis gyrata. Arch Dermatol. 1974;110(4):575-82. doi: 10.1001/archderm.110.4.575.
9. Desai SC, Sand JP, Sharon JD, Branham G, Nussenbaum B. Scalp reconstruction: an algorithmic approach and systematic review. JAMA Facial Plast Surg. 2015;17(1):56-66. doi: 10.1001/jamafacial.2014.889.
10. Moehrle M, Lischner S, Dunsche A, Breuninger H, Hauschild A. Cerebriform giant melanocytic nevus of the scalp: report of two cases with different surgical approaches. Dermatol Surg. 2002;28(1):75-9. doi: 10.1046/j.1524-4725.2002.01105.x.


Submitted date:
08/08/2020

Reviewed date:
08/31/2020

Accepted date:
09/01/2020

Publication date:
09/02/2020

5f4f7ef00e8825d71d7dc2e2 iberoamericanjm Articles
Links & Downloads

Iberoam J Med

Share this page
Page Sections